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CC BY-NC-ND 4.0 · Laryngorhinootologie 2024; 103(S 01): S125-S147
DOI: 10.1055/a-2225-9932
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Interdisziplinäres Management vaskulärer Anomalien im Kopf-Hals-Bereich

Article in several languages: deutsch | English
Stefan Mattheis
1   Klinik für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie, Universitätsmedizin Essen (Direktor: Prof. Dr. Stephan Lang)
,
Isabel Wanke
2   Zentrum für Neuroradiologie, Klinik Hirslanden, Zürich, Schweiz
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Zusammenfassung

Vaskuläre Anomalien im Kopf-Hals-Bereich sind meist seltene Erkrankungen und stellen diagnostisch und therapeutisch eine besondere Herausforderung dar. Sie werden eingeteilt in vaskuläre Tumore und vaskuläre Malformationen. Bei den Tumoren unterscheidet man benigne Tumore, wie z. B. das infantile Hämangiom. von seltenen malignen Tumoren, wie z. B. dem Angiosarkom. Die vaskulären Malformationen werden eingeteilt in einfache Malformationen, gemischte Malformationen, Anomalien großer Gefäße und Anomalien im Rahmen von Syndromen. Die Behandlung erfolgt interdisziplinär und es stehen verschiedene Modalitäten zur Verfügung. Hierzu gehören klinische Beobachtung, Sklerotherapie, Embolisation, ablative und koagulierende Verfahren, chirurgische Resektion und medikamentöse Systemtherapie. Die Therapie ist herausfordernd, da bei vaskulären Anomalien im Kopf-Hals-Bereich praktisch immer Funktion und Ästhetik betroffen sind. Ein besseres Verständnis der genetischen und molekularbiologischen Grundlagen vaskulärer Anomalien führte in jüngster Zeit zur klinischen Erforschung zielgerichteter medikamentöser Therapien. Dieser Artikel bietet eine aktuelle Übersicht über die Diagnostik, Klink und Therapie vaskulärer Anomalien im Kopf-Hals-Bereich.

Schlüsselwörter

Lymphatische Malformationen - venöse Malformationen - arterio-venöse Malformationen - Hämangiome - vaskuläre Anomalien


Publication History

Article published online:
02 May 2024

© 2024. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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