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DOI: 10.1055/s-0041-1725489
Chondrosarcoma of the Sella Turcica: Case Report and Review
Chondrosarcomas are rare, cartilage-producing, malignant mesenchymal tumors that typically develop in the bone or surrounding soft tissues. Chondrosarcomas of the midline skull base are particularly rare, with a small subset presenting as lesions of the sella and parasellar region. We present a case of chondrosarcoma presenting as a primary intrasellar mass with cavernous sinus invasion, and review the literature on chondrosarcomas of the sella, parasellar, and cavernous sinus regions.
A 57-year-old man presented with a 5-month history of progressive diplopia. On the physical examination, he was found to have a right abducens nerve palsy with intact visual acuity. Imaging demonstrated a contrast-enhancing multicystic heterogeneous mass involving the right sella turcica and cavernous sinus. The tumor was resected via an expanded endoscopic endonasal approach without complications, and histopathology was consistent with a low-grade chondrosarcoma.
Chondrosarcomas of the sella and parasellar region are particularly uncommon and may mimic pituitary adenoma in both clinical and radiographic presentation. Complete surgical resection followed by adjuvant radiotherapy is recommended due to high incidence of tumor recurrence. Albeit rare, chondrosarcoma should be included in the differential diagnosis of pituitary region masses.
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No conflict of interest has been declared by the author(s).
Publication History
Article published online:
12 February 2021
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