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DOI: 10.1055/s-0032-1315810
Fracture Healing of an Osteodysplastic Femur in a Microcephalic Osteodysplastic Primordial Dwarfism II (MOPD II) Patient: A Case Report
Publication History
08 January 2012
21 April 2012
Publication Date:
07 July 2012 (online)
Introduction
Femoral fractures are common in children. Choice of management is influenced by many factors, including age and size of the child, fracture pattern, associated injuries, and surgical and family motivations.[1] Microcephalic osteodysplastic primordial “dwarfism” type II (MOPD II) is a rare autosomal recessive condition with clinical signs of severe intrauterine and postnatal growth retardation, a progressive bony dysplasia with metaphyseal changes in the limbs and epiphyseal delay.[2] Femoral fractures in MOPD II patients have never been described. The purpose of this case report was to inform about fracture healing in this patient with dysplastic changes in the limbs.
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References
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