Tumor neuroectodérmico primitivo do terceiro ventrículo associado a metástase leptomeníngea

Resumo

Os tumores neuroectodérmicos primitivos (PNET) são tumores malignos, não diferenciados, raramente apresentados na idade adulta, principalmente os de localização supratentorial. Apresentamos neste artigo o caso de um paciente de 19 anos, que nos chegou transferido de outro hospital com o diagnóstico de hidrocefalia. A existência do PNET associado a carcinomatose leptomeníngea foi comprovada como causa da hidrocefalia.

Abstract

Primitive neuroectodermal tumors (PNET) are malignant tumors exceptionally present in adulthood, especially those with supratentorial location. In this article, we present the case of a young man who was transfer from another institution with the diagnosis of hydrocephalus; during his stay, we corroborated the presence of supratentorial PNET associated to leptomeningeal carcinomatosis that was a cause of hydrocephalus.

Palavras-Chave

tumores neuroectodérmicos primitivos - PNET - carcinomatose meníngea

Keywords

primitive neuroectodermal tumors - PNET - leptomeningeal carcinomatosis

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