Abstract
A case of marked dilatation of cerebral arteries and capillary beds associated with cyanotic congenital heart disease is reported. Computed tomography revealed many cyanosis-induced tortuous vessels in the basal cistern at 12 years old, and cerebral angiography verified the diffuse marked dilatation of main trunks, perforating arteries, and capillary beds at 15 years old. After the ventriculoperitoneal shunt was performed for the venous congestion–induced hydrocephalus, cerebral hemorrhaging occured three times, in which cyanosis-derived vasodilatation and venous hypertension were suggested to be involved.