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Klin Monbl Augenheilkd 2019; 236(04): 477-479
DOI: 10.1055/a-0829-6159
Der interessante Fall
Georg Thieme Verlag KG Stuttgart · New York

Ellipsoidopathy in Big Blind Spot Syndrome

Ellipsoidopathie bei vergrößertem blindem Fleck
Anne Bodson
1   Ophtalmologie, Hopital Ophtalmique Jules Gonin, Lausanne, Switzerland
,
François-Xavier Borruat
2   Neuro-ophtalmology, Hopital Ophtalmique Jules Gonin, Lausanne, Switzerland
› Author Affiliations
Further Information

Publication History

received 20 September 2018

accepted 15 December 2018

Publication Date:
20 February 2019 (online)

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Background

Big blind spot syndrome (BBSS) was first described by Fletcher et al. in 1988. They reported seven patients with sudden onset of photopsias and a blind spot enlargement, but an otherwise normal fundus [1]. It is a rare retinopathy, characterized by an acute loss of peripapillary outer retinal function, and occurs predominantly in young myopic women. BBSS might belong to the spectrum of occult outer retinopathies, including multiple evanescent white dot syndrome (MEWDS) [2], [3]. The mechanisms leading to BBSS and other occult outer retinopathies are speculative, but infection, vaccination, and autoimmune disorders have been implicated. The diagnosis is often difficult, mostly relying on visual field defects and electroretinographic abnormalities in the absence of clinical ocular findings.

 

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