Neurologie up2date, Table of Contents Neurologie up2date 2020; 3(04): 411-424DOI: 10.1055/a-1011-7010 Myopathien und Neuropathien Idiopathische Inflammatorische Myopathien: Klinisches Spektrum und Diagnostik Julia Wanschitz Recommend Article Abstract All articles of this category Idiopathische inflammatorische Myopathien (IIM) bzw. Myositiden sind seltene und heterogene, jedoch mit einer hohen Morbidität behaftete Erkrankungen, die eine rasche Diagnose und Therapie erfordern. Die Kernsymptome einer akuten/subakuten Muskelschwäche und Erhöhung der Creatinkinase können mit verschiedenen Begleitsymptomen einhergehen und müssen im akuten Stadium von einer Rhabdomyolyse abgegrenzt werden. Eine Antikörperdiagnostik trägt wesentlich zur Subklassifikation und Prognoseeinschätzung der Myositiden bei. Full Text References Literatur 1 Feldman BM, Rider LG, Reed AM. et al. Juvenile dermatomyositis and other idiopathic inflammatory myopathies of childhood. 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