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DOI: 10.1055/a-1739-0462
Long-Term Follow-Up of Recurrent Spontaneous Hyphema Caused by Ruptured Persistent Fetal Vasculature
Langzeitbeobachtung eines rezidivierenden Hyphämas hervorgerufen durch persistierende fötale Gefäße
Introduction
Persistent fetal vasculature (PFV) is a failure of regression of fetal intraocular vasculature during intrauterine life. Its clinical manifestation is variable among patients, depending on the subtype of PFV – anterior, posterior, or combined PFV [1], [2].
In particular, persistent pupillary membranes are part of anterior PFV. These vessels are remnants of the anterior tunica vasculosa lentis and are variably perfused from the minor arterial circle of the iris at the level of the collarette. Rarely, persistent pupillary membranes can cause recurrent hyphema in adults [3], [4], [5], [6], [7], [8].
We report the medical management and the long-term follow-up of an adult woman with recurrent spontaneous hyphema caused by a ruptured remnant of a persistent pupillary membrane.
Publication History
Received: 24 September 2021
Accepted: 09 January 2022
Article published online:
26 April 2022
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