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Klin Padiatr 2023; 235(02): 103-106
DOI: 10.1055/a-1998-6747
Short Communication

The Exception Proves the Rule: First Case of Tuberous Sclerosis-Related Pulmonary Lymphangioleiomyomatosis (LAM) in a Male Adolescent

Die Ausnahme bestätigt die Regel: Erster Fall von pulmonaler Lymphangioleiomyomatose (LAM) bei einem männlichen Jugendlichen mit tuberöser Sklerose

Authors

  • Katharina Schütz

    1   Department of Paediatric Pneumology, Allergy and Neonatology, Hannover Medical School, Hannover, Germany
  • Florian Länger

    2   Institute for Pathology, Hannover Medical School, Hannover, Germany
  • Jens Dingemann

    3   Department of Pediatric Surgery, Hannover Medical School, Hannover, Germany
  • Sandra von Hardenberg

    4   Human Genetics, Hannover Medical School, Hannover, Germany
  • Anna Zychlinsky Scharff

    5   Department of Paediatric Haematology and Oncology, Hannover Medical School Centre for Paediatrics and Adolescent Medicine, Hannover, Germany
  • Diane Renz

    6   Institute of Diagnostic and Interventional Radiology, Department of Paediatric Radiology, Hannover Medical School, Hannover, Germany
  • Tobias Welte

    7   Department of Pneumology, Hannover Medical School, Hannover, Germany
  • Nicolaus Schwerk

    8   Department of Paediatric Pneumology, Allergy and Neonatology, Hannover Medical School Centre for Paediatrics and Adolescent Medicine, Hannover, Germany
    9   BREATH (Biomedical Research in End-stage and obstructive Lung Disease Hannover), German Center for Lung Research (DZL), Hannover Medical School, Hannover, Germany