Zunehmende Luftnot und wechselnde Gelenkbeschwerden

Zusammenfassung

Bei rheumatologischen Erkrankungen soll immer die Möglichkeit einer Lungenmanifestation überprüft werden. Eine interstitielle Lungenerkrankung kann in diesen Fällen häufig letal enden. Im vorgestellten Fall ist der Zusammenhang der progredienten Dyspnoe und der neu aufgetretenen Hautirritationen als besonders wichtig zu sehen. Hier konnte durch eine rasche Therapie mit Immunsuppression und Plasmapherese ein gutes Ergebnis erzielt werden.

Abstract

In rheumatic diseases the possibility of pulmonary manifestation must always be considered and checked. Interstitial lung disease can often be fatal in these cases. In the presented case, the link between progressive dyspnea and newly occurring skin irritation is to be seen as particularly important. A good outcome can be achieved by immediate therapy with immunosuppression and plasmapheresis.

Schlüsselwörter

Dermatomyositis - interstitielle Lungenerkrankung - Plasmapherese - Immunsuppression - MDA5

Keywords

dermatomyositis - interstitial lung disease - plasmapheresis - immunosuppression - MDA5

Publication History

Received: 12 October 2022

Accepted after revision: 18 January 2023

Article published online:
23 March 2023

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