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DOI: 10.1055/a-2550-0839
Spontaneous Closure of Full-Thickness Macular Hole in a Patient with Retinal Arteriovenous Malformation: Sixteen-Year Follow-up
Spontaner Verschluss eines durchgreifenden Makulaforamens bei einem Patienten mit retinaler arteriovenöser Malformation: 16-jährige NachbeobachtungAuthors
Introduction
Retinal arteriovenous malformation (RAM), also known as retinal racemose haemangioma (RRH), is a congenital, non-hereditary, and sporadic vascular anomaly characterised by the appearance of dilated and tortuous abnormal retinal vessels. When accompanied by vascular malformations in the midbrain, mandible, or other parts of the body, it is referred to as Wyburn-Masonʼs disease [1], [2], [3].
Although RAM is typically asymptomatic and stable, complications such as central retinal vein occlusion, retinal ischaemia, and vitreous haemorrhage have been documented [4].
This report details a case of RAM complicated by central retinal vein occlusion and secondary full-thickness macular hole (FTMH) with spontaneous closure during follow-up of sixteen years.
Publication History
Accepted Manuscript online:
03 March 2025
Article published online:
16 June 2025
© 2025. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)
Georg Thieme Verlag KG
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References
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