Download PDF
Open Access
CC BY 4.0 · Aorta (Stamford) 2025; 13(05/06): 105-107
DOI: 10.1055/a-2781-8133
Case Report

Fibroinflammatory Diseases of Aorta: The Inside Look

Authors

  • Rabin Gerrah 

    1   Department of Cardiothoracic Surgery, Stanford University Cardiovascular Institute, Stanford University, Stanford, California, United States
Further Information
Also available at
  Permissions and Reprints

Abstract

Erdheim Chester disease (ECD) is a rare fibroinflammatory disease that affects different segments of aorta. It appears as diffuse wall thickening and periaortic accumulation of scar tissue on computerized tomography (CT). The CT scans describe the size and the external structure, with minimal description of endoluminal surface of the aorta. In this report, CT images were used to visualize the interior surface of the aorta and the response to treatment in a patient with ECD.

Keywords

Erdheim Chester disease - fibroinflammatory disease - aorta


Publication History

Received: 17 August 2025

Accepted: 06 January 2026

Article published online:
27 January 2026

© 2026. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Thieme Medical Publishers, Inc.
333 Seventh Avenue, 18th Floor, New York, NY 10001, USA