Skull Base 2008; 18(6): 395-399
DOI: 10.1055/s-0028-1087221
CASE REPORT

© Thieme Medical Publishers

Cerebrospinal Fluid Rhinorrhea Secondary to Ecchordosis Physaliphora

Adebayo Alli1 , Matthew Clark2 , Nicholas J. Mansell3
  • 1Department of Anatomy, Academic Centre, Henriette Raphael Building, Guy's Campus, King's College, London, United Kingdom
  • 2Department of Otolaryngology, John Radcliffe Hospital, Oxford, United Kingdom
  • 3Department of Otolaryngology, Royal Berkshire Hospital, Reading, Berkshire, United Kingdom
Further Information

Publication History

Publication Date:
07 October 2008 (online)

ABSTRACT

Ecchordosis physaliphora is a rare hamartomatous lesion of notochord origin that is usually asymptomatic. In this case report, such a lesion arose at the clivus, with extension through to the sphenoid sinus. As a result, it presented with cerebrospinal fluid rhinorhea, making the case particularly unusual. We describe the treatment for this rare situation and discuss its differentiation from chordoma, its malignant counterpart.

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Dr. Adebayo AlliM.B.B.Ch. 

Honorary Anatomy Demonstrator, Department of Anatomy, Academic Centre, Henriette Raphael Building

Guy's Campus, King's College, London SE1 1UL, United Kingdom

Email: bayoalli@doctors.org.uk