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DOI: 10.1055/s-0028-1087221
© Thieme Medical Publishers
Cerebrospinal Fluid Rhinorrhea Secondary to Ecchordosis Physaliphora
Publikationsverlauf
Publikationsdatum:
07. Oktober 2008 (online)
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ABSTRACT
Ecchordosis physaliphora is a rare hamartomatous lesion of notochord origin that is usually asymptomatic. In this case report, such a lesion arose at the clivus, with extension through to the sphenoid sinus. As a result, it presented with cerebrospinal fluid rhinorhea, making the case particularly unusual. We describe the treatment for this rare situation and discuss its differentiation from chordoma, its malignant counterpart.
KEYWORDS
Ecchordosis physaliphora - chordoma - intradural chordoma - notochord - cerebrospinal fluid
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Dr. Adebayo AlliM.B.B.Ch.
Honorary Anatomy Demonstrator, Department of Anatomy, Academic Centre, Henriette Raphael Building
Guy's Campus, King's College, London SE1 1UL, United Kingdom
eMail: bayoalli@doctors.org.uk