Thorac Cardiovasc Surg 2010; 58(6): 364-366
DOI: 10.1055/s-0029-1240551
Case Reports

© Georg Thieme Verlag KG Stuttgart · New York

Right Ventricular Outflow Obstruction of the Patient with Biventricular Non-Compaction

B. H. Sirin1 , A. T. Kurdal1 , I. Iskesen1 , M. Cerrahoglu1
  • 1Cardiovascular Surgery, Celal Bayar University, Medical Faculty, Manisa, Turkey
Further Information

Publication History

received June 24, 2009

Publication Date:
07 September 2010 (online)

Abstract

We present a case of a 16-year-old girl who underwent infundibular myectomy for right ventricular outflow tract obstruction complicated by biventricular non-compaction. The pathogenesis of this condition remains unknown. In pediatric patients non-compaction cardiomyopathy is associated with other cardiac abnormalities and carries a high mortality as a result of heart failure. In view of her improved cardiac performance after operation, we believe that a cardiac repair procedure should be performed based on the usual indications if left ventricular function is preserved.

References

  • 1 Weiford B C, Subbarao V D, Mulhern K M. Noncompaction of the ventricular myocardium.  Circulation. 2004;  109 2965-2971
  • 2 Burke A, Mont R, Kutys R, Virmani R. Left ventricular noncompaction: a pathological study of 14 cases.  Human Pathology. 2005;  36 403-411
  • 3 Jenni R, Oechslin E, Schneider J, Attenhofer Jost C, Kaufmann P A. Echocardiographic and pathoanotomical characteristics of isolated noncompaction: a step towards classification as a distinct cardiomyopathy.  Heart. 2001;  86 666-671
  • 4 Shimamoto T, Marui A, Yamanaka K et al. Left ventricular restoration surgery for isolated left ventricular noncompaction: report of the first successful case.  J Thorac Cardiovasc Surg. 2007;  134 246-247
  • 5 Ohki S, Moriyama Y, Mohara J, Kimura C, Sata N, Miyahara K. Aortic valve replacement for aortic regurgitation in a patient with left ventricular noncompaction.  Ann Thorac Surg. 2009;  87 290-292
  • 6 Chin T K, Perloff J K, Williams R G, Jue K, Mohrmann R. Isolated noncompaction of the left ventricular myocardium: a study of eight cases.  Circulation. 1990;  82 507-513
  • 7 Anderson R H. Ventricular non-compaction – a frequently ignored finding?.  Eur Heart J. 2008;  29 10-11
  • 8 Maron B J, Towbin J A, Thiene G, Antzelevitch C, Corrado D, Arnett D, Moss A J, Seidman C E, Young J B. American Heart Association; Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups. Council on Epidemiology and Prevention. Contemporary definitions and classification of the cardiomyopathies: an American Heart Association Scientific Statement from the Council on Clinical Cardiology, Heart Failure and Transplantation Committee; Quality of Care and Outcomes Research and Functional Genomics and Translational Biology Interdisciplinary Working Groups; and Council on Epidemiology and Prevention.  Circulation. 2006;  113 1807-1816
  • 9 Park J S, Shin D G, Kim Y J, Hong G R, Kim W, Lee S H, Shim B S. Left ventricular noncompaction with a single coronary artery of anomalous origin.  Int J Cardiol. 2007;  119 35-37

Dr. Adnan Taner Kurdal

Celal Bayar Tip Fakültesi Kalp ve Damar Cerrahisi
Celal Bayar University

45010 Manisa

Turkey

Phone: +90 23 62 32 58 89/1 53

Email: doktoratk@hotmail.com