Skull Base 2010; 20(3): 213-217
DOI: 10.1055/s-0029-1246224
CASE REPORT

© Thieme Medical Publishers

Ewing's Sarcoma of the Petrous Temporal Bone: Case Report and Literature Review

Aleem A. Kadar1 , Matthew J. Hearst1 , Margaret H. Collins2 , Francesco T. Mangano1 , 3 , Ravi N. Samy1 , 3
  • 1Department of Otolaryngology—Head and Neck Surgery, University of Cincinnati Neuroscience Institute and UC College of Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio
  • 2Division of Pathology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio
  • 3Department of Neurosurgery, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio
Further Information

Publication History

Publication Date:
12 January 2010 (online)

ABSTRACT

Ewing's sarcoma, which accounts for 6 to 9% of malignant bone neoplasms in children, typically affects the trunk and long bones and less often affects the skull (i.e., maxilla, frontal, parietal, ethmoid, temporal bones). Adding to literature of five previously reported cases, we now describe the case of the oldest child, a 16-year-old boy, with a primary Ewing's sarcoma of the petrous temporal bone. When this patient presented after 1 week of right-sided facial paralysis and new-onset headache, imaging studies showed a mass that originated in the right petrous temporal bone. During biopsy and surgical excision, the mass was found to involve the facial nerve, which then required nerve grafting. Postoperatively, he then underwent radiotherapy with both induction and adjuvant chemotherapy. Although an uncommon tumor of the temporal bone, physicians should consider Ewing's sarcoma in the differential diagnosis of children and adolescents who present with facial nerve paralysis.

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Ravi N SamyM.D. 

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