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DOI: 10.1055/s-0030-1250158
© Georg Thieme Verlag KG Stuttgart · New York
Early Surgical Management of Chylothorax Complicated by Gorham's Disease
Publikationsverlauf
received May 23, 2010
Publikationsdatum:
25. November 2010 (online)
Abstract
Gorham's disease is a rare disorder and its etiology remains unknown. It is characterized by the proliferation of vascular structures in bone, and results in progressive osteolysis. Chylothorax is a severe complication of Gorham's disease with a mortality of 50 %. We report a 14-year-old boy with Gorham's disease complicated by chylothorax who underwent early surgical management followed by radiotherapy.
Key words
Gorham's disease - chylothorax - thoracic duct ligation
References
- 1 Gorham L W, Stout A P. Massive osteolysis (acute spontaneous absorption of bone, phantom bone, disappearing bone). J Bone Joint Surg [Am]. 1955; 37 985-1004
- 2 Patel D V. Gorham's disease or massive osteolysis. Clin Med Res. 2005; 3 65-74
- 3 Tie M L, Poland G A, Rosenow E C. Chylothorax in Gorham's syndrome. A common complication of a rare disease. Chest. 1994; 105 208-213
- 4 Pfleger A, Schwinger W, Maier A et al. Gorham-Stout syndrome in a male adolescent – case report and review of the literature. J Pediatr Hematol Oncol. 2006; 28 231-233
- 5 Avelar R L, Martins V B, Antunes A A et al. Use of zoledronic acid in the treatment of Gorham's disease. Int J Pediatr Otorhinolaryngol. 2010; 74 319-322
Dr. Eungbae Lee, MD, PhD
Department of Thoracic and Cardiovascular Surgery
Kyungpook National University Hospital
200 Dongduk-ro Jung-gu
Daegu 700-721
Republic of Korea
Telefon: +82 5 34 20 56 65
Fax: +82 5 34 26 47 65
eMail: bay@knu.ac.kr