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DOI: 10.1055/s-0030-1250342
© Georg Thieme Verlag KG Stuttgart · New York
Primary Cardiac Lymphoma Causing Right Atrial Occlusion
Publikationsverlauf
received June 23, 2010
Publikationsdatum:
08. April 2011 (online)
![](https://www.thieme-connect.de/media/thoracic/201103/lookinside/thumbnails/10.1055-s-0030-1250342-1.jpg)
Abstract
Primary cardiac lymphomas (PCL) are extremely rare, and diffuse large B-cell lymphoma is a highly aggressive subtype. We report a case that was initially diagnosed as chronic right heart dysfunction. Detailed investigations revealed a large lobulated tumour occluding the right atrium, infiltrating the inter-atrial septum, the roof of the left atrium, and the aortic root. Despite adequate surgical debulking and initial successful tricuspid annuloplasty, the patient succumbed to multi-organ failure. Pathological analysis of the resected tumour confirmed a diffuse large B-cell lymphoma with a proliferation rate of 100 %. What is unique about this case is the size of this rare cardiac tumour, which we believe to be one of the largest described in the literature for a purely intra-cardiac PCL, its aggressive growth rate, and the relatively mild symptomatology until a late stage of the disease.
Key words
Heart disease - cardiovascular surgery - cardiomyopathy
References
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Dr. Mustafa Cikirikcioglu, M.D., Ph.D.
Department of Cardiovascular Surgery
University Hospital of Geneva
Rue Gabrielle-Perret-Gentil 4
1211 Geneva
Switzerland
Telefon: +41 7 65 35 10 84
Fax: +41 2 23 72 76 35
eMail: mustafa.cikirikcioglu@hcuge.ch