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Eur J Pediatr Surg 2012; 22(02): 171-173
DOI: 10.1055/s-0031-1286341
DOI: 10.1055/s-0031-1286341
Case Gallery
Herlyn-Werner-Wunderlich Syndrome: Uterus Didelphys, Obstructed Hemivagina, and Ipsilateral Renal Agenesis–Role of Sonographically Guided Minimally Invasive Vaginal Surgery
Further Information
Publication History
12 April 2011
16 July 2011
Publication Date:
02 November 2011 (online)
![](https://www.thieme-connect.de/media/ejps/201202/lookinside/thumbnails/10.1055-s-0031-1286341-1.jpg)
Introduction
The Mullerian ducts are the primordium from which the female reproductive tract is derived. Aberrations in Mullerian duct development such as non fusion, mal-development, defective canalisation of the ducts and failure of uterovaginal septum regression results in a wide spectrum of congenital anomalies of the female reproductive system. The estimated prevalence is 1% in women with normal fertility, with rates rising to as high as 3% in women with repeated pregnancy loss.[1] In this case report, we present a rare variant of a class 3 Mullerian duct anomaly (MDA), known as Herlyn-Werner-Wunderlich syndrome (HWWS) in a 12-year-old girl.
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References
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