Eisenmenger Syndrome Complicated by Pulmonary Artery Dissection

Abstract

This report describes a 40-year-old male patient diagnosed with pulmonary artery dissection involving both the left and right branches. The patient also had Eisenmenger syndrome secondary to an uncorrected patent ductus arteriosus. Diagnosis was facilitated through the use of transthoracic echocardiography and computed tomography. Due to the lack of definite guidelines for the optimal treatment strategy of this condition together with the poor condition of the patient, medical management was elected. Not surprisingly, the patient died suddenly only 7 days after the presentation.

Keywords

cardiac - congenital heart disease - CHD - echocardiography (all modalities, applications)

• References

• 1 Inayama Y, Nakatani Y, Kitamura H. Pulmonary artery dissection in patients without underlying pulmonary hypertension. Histopathology 2001; 38 (5) 435-442
• 2 Deterling Jr RA, Clagett OT. Aneurysm of the pulmonary artery; review of the literature and report of a case. Am Heart J 1947; 34 (4) 471-499
• 3 Khattar RS, Fox DJ, Alty JE, Arora A. Pulmonary artery dissection: an emerging cardiovascular complication in surviving patients with chronic pulmonary hypertension. Heart 2005; 91 (2) 142-145
• 4 Graham JK, Shehata B. Sudden death due to dissecting pulmonary artery aneurysm: a case report and review of the literature. Am J Forensic Med Pathol 2007; 28 (4) 342-344
• 5 Sardesai SH, Marshall RJ, Farrow RJ, Mourant AJ. Dissecting aneurysm of the pulmonary artery in a case of unoperated patent ductus arteriosus. Eur Heart J 1990; 11 (7) 670-673