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DOI: 10.1055/s-0032-1323161
Bilateral Congenital Diaphragmatic Hernia with Delayed Diagnosis
Publication History
09 May 2012
04 June 2012
Publication Date:
17 August 2012 (online)
![](https://www.thieme-connect.de/media/ejps/201304/lookinside/thumbnails/10.1055-s-0032-1323161-1.jpg)
Introduction
Congenital diaphragmatic hernia (CDH) occurs in 1 in 2500 live births and in 85% of cases the defect is left-sided. This congenital anomaly can almost always be picked up with prenatal ultrasound screening.
Bilateral hernia is extremely rare, and accounts for 2% of CDH.[1] The survival in the few reported cases is less than 30%, and that results from the greater lung hypoplasia and the greater likelihood of associated anomalies.[2] [3]
The authors present a case of a child with bilateral CDH undetected during gestation and early newborn period. The diagnosis was made in stages, during a prolonged intensive care unit stay.
The diagnosis of the right defect was deferred until 3 weeks after birth, after protracted respiratory pathology and following treatment forStreptococcus agalactiae sepsis. The left defect was diagnosed during a relaparotomy for jaundice and exploration of the bile ducts. The authors describe the diagnostic work-up and the management that resulted in an unexpectedly favorable outcome.
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References
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- 2 Furuta Y, Nakamura Y, Miyamoto K. Bilateral congenital posterolateral diaphragmatic hernia. J Pediatr Surg 1987; 22 (2) 182-183
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