Post-test

Post-test

1. OK-432 sclerotherapy appears to be most eff ective in which type of lymphatic malformation?

   • Macrocystic

   • Microcystic

   • Mixed

   • Equally eff ective in all types of lymphatic malformation

2. Patients with lymphatic malformations are at increased risk of which of the following immunodefi ciencies?

   • Neutropenia

   • Agammaglobulinemia

   • Lymphocytopenia

   • Severe combined immunodefi ciency

3. Which of the following are the accepted criteria for PHACE syndrome?

   • Pedal edema, hemihypertrophy, ankle anomaly, cardiomyopathy, ear anomaly

   • Peripheral vascular disease, hemifacial anomaly, arteriovenous malformation, cancer, eczema

   • Posterior fossa or other central nervous system malformation, hemangioma (segmental), arterial anomalies, cardiac anomalies, eye anomalies

   • Ptosis, hemorrhage, asymmetrical face, cellulitis, erysipelas

4. What drug is currently used for the treatment of hemangiomas requiring medical intervention and was discovered serendipitously for this indication?

   • Aspirin

   • Propranolol

   • Lovenox

   • Rapamycin

5. What is the name for a benign vascular lesion that grows in utero, is present at birth, and gradually involutes postnatally?

   • Hereditary hemorrhagic telangiectasia

   • Sturge-Weber syndrome

   • RICH

   • Klippel-Trenaunay syndrome

6. Which of the following lesions characteristically show GLUT-1 positivity with immunohistochemistry, helping to distinguish it from other vascular lesions of infancy?

   • Rapidly involuting congenital hemangioma

   • Noninvoluting congenital hemangioma

   • Infantile hemangioma

   • Pyogenic granuloma

7. All of these lesions are vascular tumors, except:

   • kaposiform hemangioendothelioma

   • cystic hygroma

   • tufted angioma

   • infantile hemangioma

8. Which of the following vascular anomalies are typically associated with Kasabach-Merritt syndrome?

   • Infantile hemangioma

   • Port-wine stain

   • Venous malformation

   • Tufted angioma

9. After the history and physical examination are completed, what is the initial diagnostic step for a patient with a suspected vascular lesion of the airway?

   • Ultrasound with color fl ow Doppler

   • Computed tomography scan of the head, neck, and chest

   • Magnetic resonance imaging scan of the head, neck, and chest

   • Flexible fi beroptic laryngoscopy

10. Sclerosis of lymphatic malformations involving the airway

    • usually occurs in an unmonitored, offi ce-type setting

    • involves the injection of propranolol

    • is eff ective for macro- but not microcystic lesions

    • is unnecessary due to high propensity to spontaneously resolve