Chronic Calcific Constrictive Pericarditis Complicating Churg–Strauss Syndrome: First Reported Case

Abstract

Churg–Strauss syndrome is a necrotizing systemic vasculitis characterized by extravascular granulomas and eosinophilic infiltrates of small vessels. Although cardiac complications are considered to be relatively common, no case of constrictive calcified pericarditis has ever been previously described in this setting. In this report, we present the case of a 46-year-old man with Churg–Strauss syndrome, in whom we were able to document the development of symptomatic calcific constrictive pericarditis during a 10-year period despite long-term corticosteroid therapy.

Keywords

churg–strauss syndrome - calcific constrictive pericarditis - computed tomography scan

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