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Int Arch Otorhinolaryngol 2015; 19(03): 266-268
DOI: 10.1055/s-0034-1387164
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Wegener Granulomatosis: Otologic Manifestation as First Symptom

Carla Fabiane da Costa
1   Department of Otorhinolaryngology, Hospital Universitario Evangelico de Curitiba, Curitiba, PR, Brazil
,
Jose Fernando Polanski
1   Department of Otorhinolaryngology, Hospital Universitario Evangelico de Curitiba, Curitiba, PR, Brazil
› Author Affiliations
Further Information

Publication History

09 May 2014

01 July 2014

Publication Date:
11 November 2014 (online)

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Abstract

Introduction Wegener granulomatosis is a systemic vasculitis affecting small and medium-sized vessels of the upper and lower respiratory tract and kidneys.

Objective To describe a case of Wegener disease with atypical manifestation.

Resumed Report We describe the case of a 50-year-old woman with chronic otitis media and sensorineural hearing loss as the primary symptoms, without other manifestations.

Conclusion In cases of acute ear manifestations with or without hearing loss and with poor response to usual treatments, Wegener granulomatosis should be included among the possible etiologies. After adequate diagnoses and treatment of this rare disease, there was favorable evolution.

Keywords

Wegener granulomatosis - otitis media - hearing loss
 

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