Leiomyosarcoma of the Hand

Abstract

Soft-tissue sarcomas of the hand are rare and the devastating effect of an undiagnosed sarcoma warrants clinical vigilance. We present the case of an unsuspected leiomyosarcoma localised in the hand in order to underline (i) the rarity of the disease in this site, (ii) the role of adequate surgical treatment in the first step, (iii) the relationship with adjuvant treatments, lymph node metastasis and the poor prognosis of this tumour.

Zusammenfassung

Weichteilsarkome der Hand sind selten und die verheerenden Folgen eines nicht-diagnostizierten Sarkoms mahnen zu klinischer Wachsamkeit. Wir stellen den Fall eines unerwarteten Leiomyosarkoms, dar um folgendes zu unterstreichen: 1) die Seltenheit der Krankheit an dieser Stelle 2) die Bedeutung der adäquaten chirurgischen Behandlung im Anfangsstadium 3) das Verhältnis zu Zusatzbehandlungen, Lymphknotenmetastasen und die schlechte Prognose dieses Tumors.

Key words

tumour - amputation - histology - lymphatic vessels

Schlüsselwörter

Tumor - Amputation - Histologie - Lymphgefäße

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