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Indian Journal of Neurosurgery 2015; 04(01): 031-034
DOI: 10.1055/s-0035-1548997
Case Report
Neurological Surgeons' Society of India

Intracranial Mesenchymal Chondrosarcoma: A Case Report

Prachi Agrawal
1   Department of Radiotherapy, Safdarjung Hospital, New Delhi, India
,
Ajay Gupta
1   Department of Radiotherapy, Safdarjung Hospital, New Delhi, India
,
Shagun Juneja
1   Department of Radiotherapy, Safdarjung Hospital, New Delhi, India
,
Veena Gupta
1   Department of Radiotherapy, Safdarjung Hospital, New Delhi, India
› Author Affiliations
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Publication History

Publication Date:
21 March 2015 (online)

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Abstract

Primary intracranial mesenchymal chondrosarcoma is an extremely rare tumor. We present a case of primary intracranial mesenchymal chondrosarcoma in a young female who presented with headache, loss of vision, and one episode of convulsions associated with nausea and vomiting. MRI brain revealed a large, well-marginated, lobulated, partially calcified, intensely enhancing lesion with a broad dural base in bilateral frontal regions with marked mass effect suggestive of meningioma. Bilateral frontal craniotomy with gross tumor excision was performed. Histopathology revealed mesenchymal chondrosarcoma. Adjuvant radiotherapy was delivered and patient is currently on follow-up. We emphasize that intracranial mesenchymal chondrosarcoma is a rare neoplasm and should be considered in the differential diagnoses of intracranial mass along with meningioma. Treatment of choice is surgery followed by adjuvant radiotherapy. We review the relevant literature and discuss the characteristics of this rare tumor.

Keywords

mesenchymal chondrosarcoma - intracranial - surgery - radiotherapy

Presentation at a Meeting

None.


 

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