Multimodality Renal Failure in a Patient with OEIS Complex

Jonathan D. Santoro; Stephanie Chao; Michael H. Hsieh; Henry C. Lee

doi:10.1055/s-0035-1554799

American Journal of Perinatology Reports, Table of Contents

AJP Rep 2015; 05(02): e161-e164
DOI: 10.1055/s-0035-1554799

Case Report

Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Multimodality Renal Failure in a Patient with OEIS Complex

Jonathan D. Santoro

¹Department of Pediatrics, Stanford University School of Medicine, Palo Alto, California

,

Stephanie Chao

²Department of Surgery, Stanford University School of Medicine, Palo Alto, California

,

Michael H. Hsieh

³Department of Urology, Children's National Health System, Washington, District of Columbia

,

Henry C. Lee

⁴Division of Neonatology, Department of Pediatrics, Stanford University School of Medicine, Palo Alto, California

› Author Affiliations

Abstract

Omphalocele-exstrophy of the bladder-imperforate anus-spinal defect (OEIS) complex is a rare constellation of clinical abnormalities with wide phenotypic presentation. We describe a case of a preterm neonate with OEIS complex with acute renal failure, and the challenges in diagnosis and management of this patient as renal failure can be a multifactorial process when encountered with this rare complex.

Keywords

OEIS - renal injury - genitourinary - obstructive nephropathy

Full Text

References

References
1 Carey JC, Greenbaum B, Hall BD. The OEIS complex (omphalocele, exstrophy, imperforate anus, spinal defects). Birth Defects Orig Artic Ser 1978; 14 (6B) 253-263
2 Feldkamp ML, Botto LD, Amar E , et al. Cloacal exstrophy: an epidemiologic study from the International Clearinghouse for Birth Defects Surveillance and Research. Am J Med Genet C Semin Med Genet 2011; 157C (4) 333-343
3 Hurwitz RS, Manzoni GA, Ransley PG, Stephens FD. Cloacal exstrophy: a report of 34 cases. J Urol 1987; 138 (4 Pt 2) 1060-1064
4 Muecke EC. The role of the cloacal membrane in extrosphy: the first successful experimental study. J Urol 1964; 92: 659-667
5 Phillips TM, Salmasi AH, Stec A, Novak TE, Gearhart JP, Mathews RI. Urological outcomes in the omphalocele exstrophy imperforate anus spinal defects (OEIS) complex: experience with 80 patients. J Pediatr Urol 2013; 9 (3) 353-358
6 Mukherjee B, McCauley E, Hanford RB, Aalsma M, Anderson AM. Psychopathology, psychosocial, gender and cognitive outcomes in patients with cloacal exstrophy. J Urol 2007; 178 (2) 630-635 , discussion 634–635
7 Duhamel B. Embryology of exomphalos and allied malformations. Arch Dis Child 1963; 38 (198) 142-147
8 van der Putte SCJ, Spliet WGM, Nikkels PG. Common (“classical”) and covered cloacal exstrophy: a histopathological study and a reconstruction of the pathogenesis. Pediatr Dev Pathol 2008; 11 (6) 430-442
9 Hong R, Lim SC, Jang JW , et al. OEIS complex with glomerulocystic kidney disease: a case report. Pediatr Dev Pathol 2007; 10 (2) 121-124
10 McCune TR, Stone WJ, Breyer JA. Page kidney: case report and review of the literature. Am J Kidney Dis 1991; 18 (5) 593-599