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CC BY-NC-ND 4.0 · Indian Journal of Neurosurgery 2016; 05(01): 055-058
DOI: 10.1055/s-0036-1572375
Images in Neurosurgery

Cerebral Medulloepithelioma: A Rare Aggressive Brain Tumor in Child – A Case Report

Rohit Bansil
1   Department of Neurosurgery, PGIMER and Dr. RML Hospital, New Delhi, India
,
Aman Kindra
1   Department of Neurosurgery, PGIMER and Dr. RML Hospital, New Delhi, India
,
Nasim Mansoori
2   Department of Neurosurgery, All India Institute of Medical Sciences,New Delhi, India
,
Sumit Sinha
2   Department of Neurosurgery, All India Institute of Medical Sciences,New Delhi, India
,
Suryanarayanan Bhaskar
1   Department of Neurosurgery, PGIMER and Dr. RML Hospital, New Delhi, India
,
Poojan Agarwal
3   Department of Pathology, PGIMER and Dr RML Hospital, New Delhi, India
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Abstract

Medulloepithelioma of the central nervous system (CNS) is a rare primitive neuroectodermal tumor (PNET) usually occurring in early childhood. It is a highly aggressive tumor with poor outcomes despite aggressive treatment. The ideal treatment appears to be gross total surgical resection, followed by radiation therapy. We report a case of a cerebral medulloepithelioma in a child with an aggressive tumor growth despite the gross total resection, who is surviving 1 year after diagnosis.

Keywords

cerebral medulloepithelioma - tumor - brain - child


Publication History

Received: 28 July 2015

Accepted: 23 November 2015

Publication Date:
24 February 2016 (online)

© 2016. Thieme. All rights reserved.

Neurological Surgeons' Society of India

 

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