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J Brachial Plex Peripher Nerve Inj 2016; 11(01): e48-e54
DOI: 10.1055/s-0036-1594010
Review Article
Georg Thieme Verlag KG Stuttgart · New York

Large Cervical Vagus Nerve Tumor in a Patient with Neurofibromatosis Type 1 Treated with Gross Total Resection: Case Report and Review of the Literature

David P. Bray   *
1   Department of Neurological Surgery, Columbia University, New York, New York, United States
,
Andrew K. Chan   *
2   Department of Neurological Surgery, University of California, San Francisco, California, United States
,
Cynthia T. Chin
3   Department of Neuroradiology, University of California, San Francisco, California, United States
,
Line Jacques
2   Department of Neurological Surgery, University of California, San Francisco, California, United States
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Publikationsverlauf

17. Mai 2016

04. Oktober 2016

Publikationsdatum:
16. November 2016 (online)

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Abstract

Neurofibromas are benign peripheral nerve sheath tumors that occur commonly in individuals with neurocutaneous disorders such as neurofibromatosis type 1. Vagal nerve neurofibromas, however, are a relatively rare occurrence. We present the case of a 22-year-old man with neurofibromatosis type 1 with a neurofibroma of the left cervical vagal nerve. The mass was resected through an anterior approach without major event. In the postoperative course, the patient developed left vocal cord paralysis treated with medialization with injectable gel. We then present a comprehensive review of the literature for surgical resection of vagal nerve neurofibromas.

Keywords

vagus nerve tumor - cervical vagus nerve - neurofibromatosis type 1 - neurofibroma - neck mass - diffusion tensor imaging

* David P. Bray and Andrew K. Chan contributed equally into this article.


 

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