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CC BY-NC-ND 4.0 · Indian Journal of Neurosurgery 2017; 06(03): 206-209
DOI: 10.1055/s-0036-1596042
Case Report
Thieme Medical and Scientific Publishers Private Ltd.

Epithelioid Hemangioendothelioma of Cavernous Sinus

Raj S. Chandran
1   Department of Neurosurgery, Government Medical College Thiruvananthapuram, Thiruvananthapuram, Kerala, India
,
Jyotsna Nair
2   Department of Pathology, Government Medical College Thiruvananthapuram, Thiruvananthapuram, Kerala, India
,
Krishna Balachandran
2   Department of Pathology, Government Medical College Thiruvananthapuram, Thiruvananthapuram, Kerala, India
,
Bhanu Prabhakar Rajmohan
1   Department of Neurosurgery, Government Medical College Thiruvananthapuram, Thiruvananthapuram, Kerala, India
› Author Affiliations
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Publication History

09 April 2015

17 September 2016

Publication Date:
09 May 2017 (online)

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Abstract

Epithelioid hemangioendothelioma is an uncommon vascular neoplasm. It is rare in the intracranial location. Its occurrence in the region of cavernous sinus is reported only once. Here, we report a case of 49-year-old man who presented with a headache, pain in the right eye, diplopia, and ptosis due to third and sixth cranial nerve involvement. Imaging showed an enhancing lesion in the region of cavernous sinus on the right side. Pterional craniotomy, combined extradural and intradural approach, and subtotal excision of the tumor was done. Histopathology and immunohistochemistry were suggestive of epithelioid hemangioendothelioma which is a rare tumor in this location. We report this case because of its rarity and uncommon location.

Keywords

epithelioid - hemangioendothelioma - cavernous sinus
 

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