Congenital vena cava inferior agenesis

M. Zaniewski; T. Urbanek; J. Kostecki

doi:10.1055/s-0037-1617287

Phlebologie, Table of Contents

Phlebologie 2004; 33(04): 128-130
DOI: 10.1055/s-0037-1617287

Original Articles

Schattauer GmbH

Congenital vena cava inferior agenesis

Thrombosis of the deep veins of the lower extremities with concomitant iliac, portal and mesenteric vein thrombosisAngeborene Agenesie der unteren Hohlvenen: tiefe Beinvenenthrombose bei gleichzeitiger Thrombose der Beckenvene, Pfortader und Vena mesentericaThrombose der tiefen Venen der unteren Extremitäten mit gleichzeitiger Becken-, Portal- und MesenterialvenenthromboseAgénésie congénital de la veine cave inférieure: la phlébothrombose profonde des membres inférieurs avec la thrombose des veines iliaques, de veine porte et de veine mésentériqueThrombose des veines profondes des membres inférieurs avec thrombose iliaque, portale et mésentérique concomitante

M. Zaniewski

Department of Surgery (Head: Maciej Zaniewski MD, PhD), Medical University of Silesia, District Specialist Hospital, Tychy, Poland

,

T. Urbanek

Department of Surgery (Head: Maciej Zaniewski MD, PhD), Medical University of Silesia, District Specialist Hospital, Tychy, Poland

,

J. Kostecki

Department of Surgery (Head: Maciej Zaniewski MD, PhD), Medical University of Silesia, District Specialist Hospital, Tychy, Poland

› Author Affiliations

Abstract

Summary

A patient aged 25 years with lower extremity deep vein thrombosis in the course of vena cava inferior agenesis is described. This very rare malformation can be connected with chronic venous insufficiency or thrombotic complications. In such cases other congenital abnormalities should be excluded and suspicion of vena cava inferior agenesis should always be taken into consideration in young patients with idiopathic deep vein thrombosis.

Zusammenfassung

Der Fall eines 25-jährigen Patienten mit Beinvenenthrombose infolge Agenesie der unteren Hohlvene wird beschrieben. Diese sehr seltene Fehlbildung kann mit chronischer Veneninsuffizienz und thrombotischen Komplikationen in Zusammenhang stehen. In solchen Fällen sollten andere kongenitale Abnormalitäten ausgeschlossen werden. Bei jungen Patienten mit idiopatischer Venenthrombose sollte stets die Möglichkeit der Hohlvenenagenesie in Betracht gezogen werden.

Résumé

On presente le cas d’un patient agé de 25 ans présentant la phlébothrombose profonde des membres inférieurs en cours de l’agénésie de la veine cave inférieure. Cette malformation vaisseauseuses rare peut être associée à la phlébothrombose et à l’insuffisance veineuseuse chronique. Dans tous ces cas mentionnés il faut exclure les autres pathologies mais il faut prendre en consideration l’agénésie de la veine cave inférieur chez tout les patients jeunes avec la phlébothrombose idiopathique des membres inférieurs.

Keywords

Deep vein thrombosis - vena cava agenesis

Schlüsselwörter

Beinvenenthrombose - Hohlvenenagenesie

Mots clés

La phlébothrombose profonde - l’agénésie de la veine cave

Full Text

References

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