Frühkindliche Skoliosen

Zusammenfassung

Als „frühkindlich” wird jede strukturelle Skoliose, diagnostiziert in den ersten zehn Lebensjahren, bezeichnet. Die Erkenntnisse, dass unbehandelte Patienten mit frühkindlichen Skoliosen im Erwachsenenalter eine sehr hohe kardiopulmonale Morbidität und eine deutlich eingeschränkte Lebenserwartung aufweisen, haben zu einem Paradigmenwechsel der Therapieziele geführt. Die aktuellen Behandlungskonzepte fokussieren auf Optimierung der Atemfunktion und basieren auf Erhalt des Thorax- und Lungenwachstums und auf Korrektur nicht nur der Skoliose, sondern auch der Thoraxdeformität.

Summary

Early-onset scoliosis is defined as a structural curvature diagnosed before age 10 years. There is strong evidence that the natural history of untreated patients is unfavourable and associated with a high risk of cardio-pulmonary morbidity and poor quality of life. The current treatment strategies are based on preservation of lung growth and function and focus not only on curve correction but on restoration of thorax morphology and pulmonary function as well.

Schlüsselwörter

Frühkindliche Skoliose - Early Onset Skoliose

Keywords

Early-onset scoliosis

• Literatur

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