Subscribe to RSS
DOI: 10.1055/s-0037-1618438
Frühkindliche Skoliosen
Begriffsdefinition, Ätiologie, Diagnostik, Prognose, BehandlungsprinzipienEarly-onset scoliosisDefinition, etiology, diagnosis, prognosis, treatment optionsPublication History
Publication Date:
28 December 2017 (online)
Zusammenfassung
Als „frühkindlich” wird jede strukturelle Skoliose, diagnostiziert in den ersten zehn Lebensjahren, bezeichnet. Die Erkenntnisse, dass unbehandelte Patienten mit frühkindlichen Skoliosen im Erwachsenenalter eine sehr hohe kardiopulmonale Morbidität und eine deutlich eingeschränkte Lebenserwartung aufweisen, haben zu einem Paradigmenwechsel der Therapieziele geführt. Die aktuellen Behandlungskonzepte fokussieren auf Optimierung der Atemfunktion und basieren auf Erhalt des Thorax- und Lungenwachstums und auf Korrektur nicht nur der Skoliose, sondern auch der Thoraxdeformität.
Summary
Early-onset scoliosis is defined as a structural curvature diagnosed before age 10 years. There is strong evidence that the natural history of untreated patients is unfavourable and associated with a high risk of cardio-pulmonary morbidity and poor quality of life. The current treatment strategies are based on preservation of lung growth and function and focus not only on curve correction but on restoration of thorax morphology and pulmonary function as well.
-
Literatur
- 1 El-Hawary R, Akbarnia B. Early Onset scoliosis-time for consensus; Spine deformity 2015; 3: 105-106.
- 2 Skaggs DL, Guillaume T, El-Hawary R. et al. and the Members of the SRS Growing Spine Committee. Consensus Statement. Spine Deformity 2015; 3: 107
- 3 DiMeglio A, Canavese F, Charles YP. Growth and adolescent idiopathic scoliosis: when and how much?. J Pediatr Orthop 2011; 31 (1 Suppl) S28-S36.
- 4 Campbell Jr RM, Smith MD, Mayes TC. et al. The characteristics of thoracic insufficiency syndrome associated with fused ribs and congenital scoliosis. J Bone Joint Surg Am 2003; 85-A (03) 399-408.
- 5 Pehrsson K, Larsson S, Oden A, Nachemson A. Long-term follow-up of patients with untreated scoliosis. A study of mortality, causes of death, and symptoms. Spine (Phila Pa 1976) 1992; 17 (09) 1091-1096.
- 6 Karol LA, Johnston C, Mladenov K. et al. Pulmonary function following early thoracic fusion in non-neuromuscular scoliosis. J Bone Joint Surg Am 2008; 90 (06) 1272-1281.
- 7 Skaggs DL, Akbarnia BA, Flynn JM. et al. Classification of growth friendly spine implants. J Pediatr Orthop 2014; 34: 260-274.
- 8 Tanner J, Oshman D, Bahhage F, Healy M. Tanner-Whitehouse bone age reference values for North American children. J Pediatr 1997; 131 (1 Pt 1) 34-40.
- 9 Pahys JM, Samdani AF, Betz RR. Intraspinal anomalies in infantile idiopathic scoliosis: prevalence and role of magnetic resonance imaging. Spine (Phila Pa 1976) 2009; 34 (12) E434-E438.
- 10 Dobbs MB, Lenke LG, Szymanski DA. et al. Prevalence of neural axis abnormalities in patients with infantile idiopathic scoliosis. J Bone Joint Surg Am 2002; 84-A (12) 2230-2234.
- 11 Gupta P, Lenke LG, Bridwell KH. Incidence of neural axis abnormalities in infantile and juvenile patients with spinal deformity. Is a magnetic resonance image screening necessary?. Spine (Phila Pa 1976) 1998; 23 (02) 206-210.
- 12 Wynne-Davies R. Familial (idiopathic) scoliosis. A family survey. J Bone Joint Surg Br 1968; 50 (01) 24-30.
- 13 Mehta MH. The rib-vertebra angle in the early diagnosis between resolving and progressive infantile scoliosis. J Bone Joint Surg Br 1972; 54 (02) 230-243.
- 14 McMaster MJ, Ohtsuka K. The natural history of congenital scoliosis. A study of two hundred and fifty-one patients. J Bone Joint Surg Am 1982; 64 (08) 1128-1147.
- 15 Marks DS, Qaimkhani SA. The natural history of congenital scoliosis and kyphosis. Spine (Phila Pa 1976) 2009; 34 (17) 1751-1755.
- 16 Merks JH, Smets AM, Van Rijn RR. et al. Prevalence of rib anomalies in normal Caucasian children and childhood cancer patients. Eur J Med Genet 2005; 48 (02) 113-129.
- 17 Roclawski M, Sabiniewicz R, Potaz P. et al. Scoliosis in patients with aortic coarctation and patent ductus arteriosus: does standard posterolateral thoracotomy play a role in the development of the lateral curve of the spine?. Pediatr Cardiol 2009; 30 (07) 941-955.
- 18 Van Biezen FC, Bakx PA, De Villeneuve VH, Hop WC. Scoliosis in children after thoracotomy for aortic coarctation. J Bone Joint Surg Am 1993; 75 (04) 514-518.
- 19 Persson-Bunke M, Hägglund G, Lauge-Pedersen H, Wagner P, Westbrom L. Scoliosis in a total population of children with cerebral palsy. Spine 2012; 37 (12) E708-E713.
- 20 Saito N, Ebara S, Ohotsuka K. et al. Natural history of scoliosis in spastic cerebral palsy. Lancet 1998; 351-9117 1687-1692.
- 21 Müller EB, Nordwall A. Prevalence of Scoliosis in children with myelomeningocele in western Sweden. Spine 1992; 17 (09) 1097-1102.
- 22 Trivedi J, Thomson JD, Slakey JB. et al. Clinical and radiographic pedictors of scoliosis in patients with myelomeningocelle. J Bone Joint Surg Am. 2002; 84-A (08) 1389-1394.
- 23 Levy BJ, Schulz JF, Fornari ED, Wollowick AL. Complications associated with surgical repair of syndromic scoliosis. Scoliosis 2015; 10: 14
- 24 Sponseller PD, Hobbs W, Riley LH. 3rd Pyeritz RE. The thoracolumbar spine in Marfan syndrome. J Bone Joint Surg Am 1995; 77: 867-876.
- 25 Tsirikos AI, Saifuddin A, Noordeen H. Spinal deformity in neurofibromatosis type-1: diagnosis and treatment. Eur Spine J 2005; 14: 427-439.
- 26 Odent T, Accadbled F, Koureas G. et al. Scoliosis in patients with Prader-Willi Syndrome. Pediatrics 2008; 122 (02) e499-e503.