Rezidivierende Arthritiden/Arthralgien und urtikarielle Exantheme

Zusammenfassung

Bei einem 12 ¾-jährigen Mädchen mit rezidivierenden Arthritiden/Arthralgien und seit der Neugeborenenzeit auftretenden urtikariellen Exanthemen, Verzögerung der Wachstumsgeschwindigkeit, Müdigkeit und hoher humoraler Entzündungsaktivität war eine breite diagnostische Abklärung erforderlich, die u.a. die systemische juvenile idiopathische Arthritis (Still-Syndrom), die juvenile Psoriasisarthritis, Kollagenosen, Vaskulitiden, entzündliche Darmerkrankun-gen sowie periodische Fiebersyndrome umfasste.

Summary

In a 12 ¾-year-old girl with repetitive arthritides/arthralgias and with neonatal-onset urticarial rashes, delayed growth velocity, fatigue and the laboratory findings of an increased acute phase reaction the differential diagnoses included in particular systemic juvenile idiopathic arthritis, juvenile psoriatic arthritis, connective tissue diseases, vasculitides, inflammatory bowel diseases and hereditary periodic fevers.

Schlüsselwörter

Urtikaria - periodische Fiebersyndrome - Muckle-Wells-Syndrom

Keywords

Urticaria - autoinflammatory syndromes - Muckle-Wells syndrome

• Literatur

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