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Hamostaseologie 2005; 25(02): 200-204
DOI: 10.1055/s-0037-1619654
Original Article
Schattauer GmbH

Hämostaseologische Krankheitsbilder auf der Intensivstation

TTP, HUS, FVIII-Hemmkörperhämophilie und katastrophales APS-SyndromHaemostaseological diseases on the intensive care unitsTTP, HUS, spontaneous acquired FVIII inhibitor haemophilia and catastrophic antiphospholipide syndrome
I. Scharrer
1   Hämostaseologie (Leiterin: Prof. Dr. med. Inge Scharrer), J.W. Goethe Universitätskliniken Frankfurt am Main
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Publication History

Publication Date:
27 December 2017 (online)

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Zusammenfassung

Ein kleiner Teil der Intensivpatienten leiden an akuten hämostaseologischen Erkrankungen mit sehr schlechter Prognose. Zu diesen Notfallerkrankungen zählen die thrombotisch-thrombozytopenische Purpura (TTP), das hämolytisch-urämische Syndrom (HUS), die erworbene Hemmkörperhämophilie und das Catastrophic-Antiphospholipid-Syndrom (CAPS). Diese Patienten benötigen eine sehr schnelle Diagnostik und eine sofortige Therapie.

Summary

A minority of patients presenting with acute life threatening syndromes characterized by severe bleeding episodes or microvascular thromboses on the intensive care unit. Especially patients with TTP, HUS, acquired haemophilia and CAPS have a poor prognosis. These emergency cases require a rapid diagnosis and an immediate onset of treatment.

Schlüsselwörter

TTP - HUS - FVIII-Hemmkörperhämophilie - CAPS

Keywords

TTP - HUS - spontaneous acquired FVIII inhibitor haemophilia - CAPS
 

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