Kardiale Beteiligung bei hereditären und erworbenen Muskelerkrankungen

S. Neudecker; S. Zierz

doi:10.1055/s-0038-1626411

Nervenheilkunde, Table of Contents

Nervenheilkunde 2004; 23(08): 457-464
DOI: 10.1055/s-0038-1626411

Original- und Übersichtsarbeiten - Original and Review Articles

Schattauer GmbH

Kardiale Beteiligung bei hereditären und erworbenen Muskelerkrankungen

Cardiac involvement in hereditary and acquired muscle diseases

S. Neudecker

¹Klinik und Poliklinik für Neurologie, Martin-Luther-Universität Halle-Wittenberg

,

S. Zierz

¹Klinik und Poliklinik für Neurologie, Martin-Luther-Universität Halle-Wittenberg

› Author Affiliations

Abstract

Zusammenfassung

Die Skelettmuskulatur und der Herzmuskel sind zwei anatomisch eindeutig voneinander zu unterscheidende Gewebe, die dennoch verschiedene Gemeinsamkeiten aufweisen. Erkrankungen mit primärem Befall der Skelettmuskulatur können deshalb auch zur Manifestation kardialer Symptome führen und umgekehrt. Obgleich bei Myopathien häufig Paresen und Atrophien bzw. Myalgien im Vordergrund der Beschwerden stehen, können kardiale Symptome einen erheblichen Einfluss auf die Lebensqualität und -erwartung besitzen und in Einzelfällen das klinische Bild dominieren. In der vorliegenden Arbeit werden diejenigen hereditären und erworbenen Muskelkrankheiten aufgeführt, bei denen eine Herzbeteiligung bekannt ist.

Summary

Although the skeletal muscle and the heart are two anatomical distinct tissues, they have several similarities. Primary myogenic disorders may have a cardiac involvement and vice versa. Weakness, muscular atrophy and myalgias are the most important symptoms in myopathies. However, cardiac involvement in myopathies may have a wide influence on quality of life and on life expectancy. In this paper hereditary and acquired muscle diseases with cardiac involvement are presented.

Schlüsselwörter

Myopathien - hereditär - erworben - Herzbeteiligung

Keywords

Myopathies - hereditary - acquired - cardiac involvement - heart

Full Text

References

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