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Thromb Haemost 1976; 35(02): 377-381
DOI: 10.1055/s-0038-1647931
Original Article
Schattauer GmbH

Treatment of Amyloidosis Associated Factor X Deficiency

Joel A. Spero
1   Department of Medicine, University of Pittsburgh and Central Blood Bank of Pittsburgh, Pittsburgh PA 15219
,
Jessica H. Lewis
1   Department of Medicine, University of Pittsburgh and Central Blood Bank of Pittsburgh, Pittsburgh PA 15219
,
Ute Hasiba
1   Department of Medicine, University of Pittsburgh and Central Blood Bank of Pittsburgh, Pittsburgh PA 15219
,
Lawrence D. Ellis
1   Department of Medicine, University of Pittsburgh and Central Blood Bank of Pittsburgh, Pittsburgh PA 15219
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Publikationsverlauf

Received 02. Oktober 1975

Accepted 20. November 1975

Publikationsdatum:
02. Juli 2018 (online)

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Summary

This is the tenth patient in thirteen years to be reported with the findings of an isolated factor X deficiency associated with primary amyloidosis. A favorable response to factor IX concentrate was manifested by temporary clinical and laboratory correction of her diathesis. This mode of treatment, therefore, provides an approach to therapy for bleeding complications in this group of patients who have previously failed to respond to fresh frozen plasma.

 

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