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Thromb Haemost 1964; 11(02): 497-505
DOI: 10.1055/s-0038-1654845
Originalarbeiten — Original Articles — Travaux Originaux
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A Study of Three Cases of Familial Congenital Hypoprothrombinaemia (Factor II Deficiency)

O de Bastos
1   Haematological Department of the Central Laboratory of the School of Medicine, Minas Gerais University, Belo-Horizonte, Minas Gerais, Brazil
,
R. S Reno
1   Haematological Department of the Central Laboratory of the School of Medicine, Minas Gerais University, Belo-Horizonte, Minas Gerais, Brazil
,
O. T Correa
1   Haematological Department of the Central Laboratory of the School of Medicine, Minas Gerais University, Belo-Horizonte, Minas Gerais, Brazil
› Author Affiliations
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Publication History

Publication Date:
22 June 2018 (online)

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Summary

Three cases of true congenital hypoprothrombinaemia are presented.

Studies were made to prove the deficiency of prothrombin in the patient’s plasma and to rule out deficiency of other clotting factors or the presence of abnormal anti-thrombin substances.

All the patients were of group B.

The results obtained confirm that the patients have a real prothrombin deficiency as the cause of a severe haemorrhagic disease.

 

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