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CC BY-NC-ND 4.0 · AJP Rep 2018; 08(02): e138-e141
DOI: 10.1055/s-0038-1656533
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

An Unusual Neonatal Presentation of Scimitar Syndrome

Ahmad Abdul Aziz
1   Section of Neonatology, Department of Pediatric, University of Calgary, Calgary, Alberta, Canada
,
Sumesh Thomas
1   Section of Neonatology, Department of Pediatric, University of Calgary, Calgary, Alberta, Canada
,
David Lautner
2   Department of Diagnostic Imaging, Foothill Medical Centre, University of Calgary, Calgary, Alberta, Canada
,
Essa Hamadan Al Awad
1   Section of Neonatology, Department of Pediatric, University of Calgary, Calgary, Alberta, Canada
› Author Affiliations
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Publication History

20 February 2018

02 April 2018

Publication Date:
20 June 2018 (online)

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Abstract

Scimitar syndrome is characterized by partial or total anomalous pulmonary venous return from the right lung along with pulmonary hypoplasia. We present a case of a 37 weeks' gestation male infant with antenatal ultrasound findings of suspected partial anomalous pulmonary venous return (PAPVR) and coarctation of the aorta. The newborn presented with respiratory distress, a chest X-ray and chest computed tomography (CT) angiogram confirmed the diagnosis of scimitar syndrome. The combination of scimitar syndrome with aortic coarctation is extremely rare with only a few cases previously reported.

Keywords

neonatology - perinatology - pediatric cardiology - pulmonology
 

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