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Thromb Haemost 1984; 51(03): 331-333
DOI: 10.1055/s-0038-1661094
Original Article
Schattauer GmbH Stuttgart

Congenital Hemorrhagic Disorders in Jordan[*]

Abdalla S Awidi
The Department of Medicine and Hematology, Faculty of Medicine, Jordan University, Amman, Jordan
› Author Affiliations
Further Information

Publication History

Received 27 November 1983

Accepted 16 March 1984

Publication Date:
19 July 2018 (online)

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Summary

The results of a three year prospective study of inherited bleeding syndromes in Jordan is presented. There were 112 patients from 64 families. Of these there were 42 patients with hemophilia A, 23 with Glanzmann’s thrombasthenia, 22 with von Willebrand’s disease, 11 with Christmas disease, 6 with hypofibrinogenemia, 3 with afibrinogenemia, 2 with factor XIII deficiency, 2 with storage pool disease and 1 with factor XI deficiency. The pattern of inherited bleeding syndromes in Jordan is different from that seen in Europe and U.S.A. in that Glanzmann’s thrombasthenia is very common. High proportion of hemophiliacs were severe. Arthropathy was common. A significant number of bleeders had fatal hemorrhage. In a high proportion of patients, no family history of bleeding was found.

Keywords

Glanzmann’s thrombasthenia - Hemophilia - Congenital hemorrhage

* This work was supported in part by the University of Jordan in part by Mr. M. Othman and Mr. R. Goshah


 

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