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CC BY-NC-ND 4.0 · AJP Rep 2019; 09(02): e144-e146
DOI: 10.1055/s-0039-1683936
Case Report
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Pentalogy of Cantrell in Full Term Neonate

Nadereh Taee
1   Department of Pediatrics, Lorestan University of Medical Sciences, Khorramabad, Iran
,
Mojgan Faraji Goodarzi
1   Department of Pediatrics, Lorestan University of Medical Sciences, Khorramabad, Iran
,
Mohammad Safdari
2   Medical Student, Lorestan University of Medical Sciences, Khorramabad, Iran
,
Amir Bajelan
2   Medical Student, Lorestan University of Medical Sciences, Khorramabad, Iran
› Author Affiliations
Further Information

Publication History

26 April 2018

30 December 2018

Publication Date:
09 April 2019 (online)

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Abstract

Pentalogy of Cantrell (PC) is an uncommon congenital disorder characterized by severe defects in the chest and abdomen, including abdominal visceral prolapsed via umbilical cord (omphalocele), defect in the lower part of the sternum, defect in the front of the diaphragm, defects in the anterior part of the pericardium, and the ectopiacordis. Here, we report a 2-hour-old girl, weighing 3,500 g, who was referred to Shahid Madani Hospital in Khorramabad due to the large omphalocele on her chest with pulsating mass above it. The baby was the first child of a 24-year-old mother who was born with an uncomplicated vaginal delivery. Very rare cases of PC are born as a term new-born.

Keywords

Pentalogy of Cantrell - omphalocele - pulsatile mass

Compliance with Ethical Standards

Research involving human participants and/or animals–ethical approval: All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.


Informed Consent

Informed consent was obtained from all individual participants included in the study.


 

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