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CC BY-NC-ND 4.0 · Eur J Dent 2010; 04(02): 215-222
DOI: 10.1055/s-0039-1697832
Original Article
European Journal of Dentistry

Ectodermal Dysplasia with Anodontia: A Report of Two Cases

Mehmet Bani
a   Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey
,
Ali Melih Tezkirecioglu
b   Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey
,
Nese Akal
c   Gazi University, Faculty of Dentistry, Department of Paediatric Dentistry, Ankara, Turkey
,
Tamer Tuzuner
d   Karadeniz Technical University, Faculty of Dentistry, Department of Paediatric Dentistry, Trabzon, Turkey
› Author Affiliations
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Publication History

Publication Date:
30 September 2019 (online)

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Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances in the ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. Two case reports illustrating the prosthetic rehabilitation of 2 young boys with anhidrotic ectodermal dysplasia associated with severe anodontia are presented. Since the oral rehabilitation of these cases is often difficult; particularly in pediatric patients, treatment should be administered by a multidisciplinary team involving pediatric dentistry, orthodontics, prosthodontics and oral-maxillofacial surgery. (Eur J Dent 2010;4:215-222)

Keywords

Anodontia - Prosthetic rehabilitation - Multidisciplinary management
 

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