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CC BY-NC-ND 4.0 · Eur J Dent 2010; 04(03): 338-340
DOI: 10.1055/s-0039-1697849
Original Article
European Journal of Dentistry

Periodontal Manifestations in a Patient with Haim-Munk Syndrome

Kamile Erciyas
a   Gaziantep University, Faculty of Dentistry, Department of Periodontology, Gaziantep, Turkey
,
Serhat Inaloz
b   Gaziantep University, Faculty of Medicine, Department of Dermatology, Gaziantep, Turkey
,
A. Fuat Erciyas
c   Clinical of Orthodonthy, Gaziantep, Turkey
› Author Affiliations
Further Information

Publication History

Publication Date:
30 September 2019 (online)

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Haim-Munk syndrome is an extremely rare autosomal recessive disorder characterized clinically by palmoplantar hyperkeratosis, aggressive periodontitis with severe alveolar bone destruction, onychogryphosis, pes planus, arachnodactyly, and acro-osteolysis. Consanguinity seems a notable prerequisite. The aim of this study was therefore to report one case of this syndrome and to focus on the periodontal manifestations, in order to attract the attention of dental clinicians to this rare anomaly. (Eur J Dent 2010;4:338-340)

Keywords

Periodontitis - Haim-Munk syndrome - Palmoplantar keratoderma
 

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