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CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2022; 11(01): e17-e19
DOI: 10.1055/s-0041-1729928
Case Report: Thoracic

Mediastinal Rhabdomyosarcoma Feeding Off the Left Anterior Descending Artery

Milena Guenther
1   Department of Cardiothoracic Surgery, Jena University Hospital, Jena, Thüringen, Germany
,
Markus Richter
1   Department of Cardiothoracic Surgery, Jena University Hospital, Jena, Thüringen, Germany
,
Torsten Doenst
1   Department of Cardiothoracic Surgery, Jena University Hospital, Jena, Thüringen, Germany
,
Tobias Rachow
2   Department of Pneumology, Jena University Hospital, Jena, Thüringen, Germany
,
Susanne Lang
3   Department of Hematology and Internal Oncology, Jena University Hospital, Jena, Thüringen, Germany
,
Tim Sandhaus
1   Department of Cardiothoracic Surgery, Jena University Hospital, Jena, Thüringen, Germany
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Abstract

We report the rare case of a 51-year-old patient with a 15 cm mediastinal rhabdomyosarcoma with blood supply from the left anterior descending artery presenting as a large mass including the pericardium with extensive contact to the epicardium compressing heart and left lung. The tumor was successfully removed through median sternotomy, blunt dissection from the heart and the left lung, resection of the infiltrated pericardium, and ligation of the tumor-feeding vessels using off-pump stabilizers. Histopathological examination revealed a spindle cell rhabdomyosarcoma with R0 resection. The postoperative course was uneventful, and patient is feeling well at 3-month follow-up.

Keywords

mediastinal rhabdomyosarcoma - pericardium - off-pump stabilizer - surgery - complication


Publication History

Received: 23 December 2020

Accepted: 08 March 2021

Article published online:
25 February 2022

© 2022. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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