RSS-Feed abonnieren
DOI: 10.1055/s-0041-1733775
Obstructive Hydrocephalus Presenting with Bobble-Head Doll Syndrome
![](https://www.thieme-connect.de/media/neuropediatrics/202201/lookinside/thumbnails/10-1055-s-0041-1733775_212877vin-1.jpg)
A previously healthy macrocephalic 3-year-old boy presented with a 3-month-history of progressive up-and-down head movements that were increased with distraction, decreased with concentration, and voluntarily suppressed ([Video 1], Segment 1). Brain MRI showed suprasellar cystic lesion causing obstructive hydrocephalus ([Fig. 1]). He was successfully treated with endoscopic third ventriculostomy and movements abated ([Video 1], Segment 2). Bobble-head doll syndrome is a rare and surgically treatable movement disorder usually associated with dilation of the third ventricle and characterized by the up-and-down, two to three second cycles of bobbling movements of the head and neck.[1] [2]
Video 1 Segment one shows the child displaying movements typical of the bobble-head doll syndrome. At the beginning of the video the patient is able to control the movements. Then, when relaxed and talking to the examiner, the movements appear. Segment two shows a 1-year follow-up after the surgical procedure with total resolution of movements.
Qualität:
![](https://www.thieme-connect.de/media/neuropediatrics/202201/thumbnails/10-1055-s-0041-1733775-i212877vin-1.jpg)
![Zoom Image](/products/assets/desktop/css/img/icon-figure-zoom.png)
Note
This work was performed at the Hospital e Maternidade São José in Conselheiro Lafaiete, MG, Brazil.
Ethical Statement
Full consent was obtained from the patient for the case report publication.
Financial Disclosure
None.
Authors' Contribution
IAF, TCV, FLF, AVSB, worked on case report project and imaging's conception, organization, execution.
M.M.A. and M.R.M. worked on conception, organization and execution of imaging. They wrote the manuscript and worked as reviewer and critique.
Publikationsverlauf
Eingereicht: 08. März 2021
Angenommen: 24. Juni 2021
Artikel online veröffentlicht:
26. August 2021
© 2021. Thieme. All rights reserved.
Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany
-
References
- 1 Wiese JA, Gentry LR, Menezes AH. Bobble-head doll syndrome: review of the pathophysiology and CSF dynamics. Pediatr Neurol 1985; 1 (06) 361-366
- 2 Renne B, Rueckriegel S, Ramachandran S, Radic J, Steinbok P, Singhal A. Bobble-head doll syndrome: report of 2 cases and a review of the literature, with video documentation of the clinical phenomenon. J Neurosurg Pediatr 2018; 21 (03) 236-246