An Unusual Cause of Cholestasis in an Infant: Biliary Atresia Type IIB

Poonam Sherwani; Rishi Bolia; Ashish Kaushik; Sumit Kumar; Sanjeev Kishore; Udit Chauhan

doi:10.1055/s-0041-1736165

Indian Journal of Radiology and Imaging, Table of Contents

CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(03): 689-692
DOI: 10.1055/s-0041-1736165

Case Report

An Unusual Cause of Cholestasis in an Infant: Biliary Atresia Type IIB

Poonam Sherwani

¹Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

,

Rishi Bolia

²Department of Pediatrics, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

,

Ashish Kaushik

¹Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

,

Sumit Kumar

¹Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

,

Sanjeev Kishore

³Department of Pathology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

,

Udit Chauhan

¹Department of Radiodiagnosis, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India

› Author Affiliations

Abstract

Biliary atresia (BA) is a progressive destructive cholangiopathy of unknown etiology that presents in early infancy. It has a worldwide frequency of 1:8,000–1:15,000 and is common in Asia than in the west. Based on the level at which the lumen of the extrahepatic duct is obliterated, BA is classified into three types. Type III is the commonest (∼85%) type and has the most proximal level of obstruction in the porta hepatis, while type II in which the atresia is at the level of the common hepatic duct, is the least common (∼2.5%) and has been rarely reported. Here, we report the imaging features of an infant with type IIB biliary atresia.

Keywords

biliary atresia - cholangiopathy - common hepatic duct

Full Text

References

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