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CC BY-NC-ND 4.0 · Thorac Cardiovasc Surg Rep 2021; 10(01): e61-e63
DOI: 10.1055/s-0041-1736208
Case Report: Cardiac

Mitral Multifocal Papillary Fibroelastoma in a Patient with Aggressive Fibromatosis

Philipp P. Müller
1   Department of Cardiac Surgery, Friedrich–Alexander University Erlangen–Nuremberg, Erlangen, Germany
,
Abbas Agaimy
2   Institute of Pathology, Friedrich–Alexander University Erlangen–Nuremberg, Erlangen, Germany
,
Michael Weyand
1   Department of Cardiac Surgery, Friedrich–Alexander University Erlangen–Nuremberg, Erlangen, Germany
,
Christian Heim 
1   Department of Cardiac Surgery, Friedrich–Alexander University Erlangen–Nuremberg, Erlangen, Germany
› Author Affiliations Funding This publication was supported by Deutsche Forschungsgemeinschaft and University of Erlangen Foundation within the funding program Open Access Publishing.
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Abstract

Mitral valve fibroelastoma is a rare condition that can be associated with high morbidity rates due to thrombus formation and resulting embolic events. Causative treatment for affected patients is mitral valve surgery. An association between cardiac fibroelastoma and desmoid-type fibromatosis, an aggressive form of fibromatosis, is not yet described. We present a case of a 58-year-old man with a history of desmoid-type fibromatosis and concomitant papillary fibroelastoma of the mitral valve who consequently underwent mitral valve replacement.

Keyword

histology - mitral valve surgery - tumor - cardiac

Authors' Contribution

Concept/design: C.H.; data interpretation: A.A. and P.P.M.; drafting article: P.P.M.; critical revision of article: C.H.; approval of article: P.P.M., A.A., M.W., and C.H.; funding: C.H.


Institutional Review Board Waiver and Patient Consent Statement

Patient signed informed consent related to clinical course; therefore and due to its retrospective nature of the educational case report, the IRB was waived.




Publication History

Received: 30 March 2021

Accepted: 29 June 2021

Article published online:
25 December 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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