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CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2021; 40(04): e394-e398
DOI: 10.1055/s-0041-1739279
Case Report | Relato de Caso

Management and Outcome of a Neurologically Intact Infant with Pierre Robin Sequence and Dandy-Walker Variant Diagnosed with Large Hemispheric Brain Abscess – Case Report

Manejo e resultado de um bebê neurologicamente intacto com sequência de Pierre Robin e variante de Dandy-Walker diagnosticada com grande abscesso cerebral hemisférico – Relato de caso
Mohammad A. Jamous
1   Division of Neurosurgery, Department of Neuroscience, Faculty of Medicine, Jordan University of Science & Technology, Irbid, Jordan
,
Amer A. Alomari
1   Division of Neurosurgery, Department of Neuroscience, Faculty of Medicine, Jordan University of Science & Technology, Irbid, Jordan
,
Omar F. Jbarah 
1   Division of Neurosurgery, Department of Neuroscience, Faculty of Medicine, Jordan University of Science & Technology, Irbid, Jordan
› Institutsangaben Funding The present study was not funded.
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Abstract

Pierre Robin sequence (PRS) is a condition consisting of three essential components: micrognathia or retrognathia, cleft palate, and glossoptosis. It can be part of multiple congenital anomalies. We present the case and outcome of a 3-month-old clinically stable patient who has PRS with Dandy-Walker variant – which is a rare presentation in the literature – with a large right hemispheric brain abscess, treated with multiple minimally-invasive surgical drainage procedures with adjuvant antibiotics.

Resumo

A sequência de Pierre Robin (SPR) é uma condição que consiste em três componentes essenciais: micrognatia ou retrognatia, fenda palatina e glossoptose. Pode ser parte de várias anomalias congênitas. Apresentamos o caso e a evolução de um paciente clinicamente estável de 3 meses que tem PRS com variante de Dandy-Walker – uma apresentação rara na literatura – com um grande abscesso cerebral hemisférico direito, tratado com vários procedimentos de drenagem cirúrgica minimamente invasiva com antibióticos adjuvantes.

Keywords

Pierre Robin sequence - Dandy-Walker variant - brain abscess

Palavras-chave

sequência de Pierre Robin - variante Dandy-Walker - abscesso cerebral

Ethical Consideration

Written informed consent was obtained from the patient's parents for publication of the case report and any related images.




Publikationsverlauf

Eingereicht: 19. Juli 2021

Angenommen: 13. August 2021

Artikel online veröffentlicht:
26. November 2021

© 2021. Sociedade Brasileira de Neurocirurgia. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commecial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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