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CC BY 4.0 · Surg J (N Y) 2021; 07(04): e363-e365
DOI: 10.1055/s-0041-1740628
Case Report

Bochdalek Hernia and Partial Diaphragmatic Agenesis: Pedicled Intercostal Muscle Flap and Mesh Repair in a Young Adult with Sickle Cell Disease

Klein Dantis 
1   Department of Cardiothoracic Surgery, All India Institute of Medical Sciences, Raipur, Chhattisgarh, India
,
Devendra Kumar Rathore
2   Department of General Surgery, All India Institute of Medical Sciences, Raipur, Chhattisgarh, India
,
Nilesh Gupta 
3   Department of Radiodiagnosis, All India Institute of Medical Sciences, Raipur, Chhattisgarh, India
,
Subrata Kumar Singha
4   Department of Anesthesiology, All India Institute of Medical Sciences, Raipur, Chhattisgarh, India
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Abstract

Congenital Bochdalek hernia (BH) in an adult is rare and has an unusual presentation. They are confined to the pediatric age group with an incidence of 1:3,000 live births. It rarely persists asymptomatic until adulthood. Surgical repair by thoracic, abdominal, or thoraco-abdominal approach is the treatment of choice with diaphragmatic reconstruction in associated diaphragmatic agenesis. With only 10 cases of BH with partial diaphragmatic agenesis reported to date, we discuss the rarity, unusual presentation, and management of BH in a young adult with sickle cell disease that has not been reported in the literature.

Keywords

congenital diaphragmatic hernia - hemidiaphragm agenesis - sickle cell disease - intercostal muscle flap - ectopic kidney - vertebral fusion

Author Contribution

Klein Dantis prepared and drafted the manuscript. All the coauthors edited, reviewed, and accepted the manuscript.




Publication History

Received: 24 September 2021

Accepted: 09 November 2021

Article published online:
23 December 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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