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CC BY-NC-ND 4.0 · Indian J Radiol Imaging 2021; 31(04): 1057-1061
DOI: 10.1055/s-0041-1741047
Case Report

Sporadic Intradural Extramedullary Hemangioblastoma of Cauda Equina with Large Peritumoral Cyst—A Rare Presentation

Pushpa B. Thippeswamy
1   Department of Radiology, Ganga Hospital, Coimbatore, Tamil Nadu, India
,
Dilip C. R. Soundararajan
2   Department of Spine Surgery, Ganga Hospital, Coimbatore, Tamil Nadu, India
,
Ríshi M. Kanna
2   Department of Spine Surgery, Ganga Hospital, Coimbatore, Tamil Nadu, India
,
Venkata S. Kuna
1   Department of Radiology, Ganga Hospital, Coimbatore, Tamil Nadu, India
,
Shanmuganathan Rajasekaran
2   Department of Spine Surgery, Ganga Hospital, Coimbatore, Tamil Nadu, India
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Abstract

Cauda equina intradural tumors commonly reported include ependymoma, schwannoma, neurofibroma, meningioma, and drop metastasis. Hemangioblastoma of the neural axis is a rare benign vascular tumor comprising only 1.6 to 6.4% of spinal tumors, and are usually associated with Von-Hippel Lindau disease. Sporadic intradural extramedullary hemangioblastoma involving cauda equina is very rare with only countable reports, and the presence of peritumoral cyst has been reported only once. We report one such case of hemangioblastoma with a large peritumoral cyst, which was diagnosed radiologically and confirmed by histopathology following surgical excision. Pertinent radiological characteristics, diagnostic clues, treatment, and surgical outcomes are discussed.

Keywords

cauda equina tumors - cystic lesion - hemangioblastoma - intradural tumors

Financial Support and Sponsorship

Ganga Orthopedic Research and Education Foundation.




Publication History

Article published online:
10 January 2022

© 2022. Indian Radiological Association. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)

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